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Originalarbeiten, Bücher, Buchkapitel und Übersichtsartikel von Prof. Marcus Maurer
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The dermatology view of hereditary angioedema: Practical diagnostic and management considerations
| Filename | 73. Maurer Parish, The dermat. view of HAE, JEADV 2013.pdf |
| Filesize | 403,45 KB |
| Version | r.073 |
| Date added | Juni 26, 2020 |
| Downloaded | 0 times |
| Category | Reviews |
| Authors | Maurer, M and Parish, L. C. |
| Citation | Maurer, M. and Parish, L. C.: The dermatology view of hereditary angioedema: Practical diagnostic and management considerations. J. Eur. Acad. Dermatol. Venereol. 2013: 27; 133-141. |
| Corresponding authors | Maurer, M |
| DocNum | r.73 |
| DocType | |
| Edition; Page | 27; 133-141 |
| IF | 2.78 |
| Publisher | J. Eur. Acad. Dermatol. Venereol. |
| ReleaseDate | 2013 |
Hereditary angio-oedema (HAE) is characterized by recurrent, localized, non-pitting, non-pruritic, non-urticarial oedema. Nearly all patients experience skin swelling as a feature of HAE. There may be painful abdominal attacks, accompanied by nausea and vomiting. The disease is life-threatening should laryngeal oedema occur. HAE results from a deficiency or dysfunction of C1 inhibitor, a plasma protein with an important role in regulating the contact, complement and fibrinolytic systems. Effective management of HAE should include a plan for treatment of attacks, as well as routine and preprocedure prevention. Acute and prophylactic therapy with C1 inhibitor therapy for correcting the underlying deficiency in HAE is a valuable option.
Received: 19 December 2011; Accepted: 4 April 2012
(Last update: 07.2025)
| Number of original publications in peer-reviewed journals: | 650 |
| Number of reviews in peer-reviewed journals: | 229 |
| Number of publications (original work and reviews) in peer-reviewed journals: | 879 |
| Cumulative IF for original publications in peer-reviewed journals: | 4648.29 |
| Cumulative IF for reviews in peer-reviewed journals: | 1689.22 |
| Cumulative IF of publications (original work & reviews) in peer-reviewed journals: | 6761.91 |
| Total number of citations: 45.522, h-index: 109 (Web of Science Juli 2025) | 45522 |
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